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@ARTICLE{Lapkouski:276466,
author = {Lapkouski, Mikalai and Haellberg, Martin},
title = {{S}tructure of mitochondrial poly({A}) {RNA} polymerase
reveals the structural basis for dimerization, {ATP}
selectivity and the {SPAX}4 disease phenotype.},
journal = {Nucleic acids symposium series},
volume = {43},
number = {18},
issn = {1362-4962},
address = {Oxford},
publisher = {Oxford Univ. Press8619},
reportid = {PUBDB-2015-04674},
pages = {9065 - 9075},
year = {2015},
abstract = {Polyadenylation, performed by poly(A) polymerases (PAPs),
is a ubiquitous post-transcriptional modification that plays
key roles in multiple aspects of RNA metabolism. Although
cytoplasmic and nuclear PAPs have been studied extensively,
the mechanism by which mitochondrial PAP (mtPAP) selects
adenosine triphosphate over other nucleotides is unknown.
Furthermore, mtPAP is unique because it acts as a dimer.
However, mtPAPs dimerization requirement remains enigmatic.
Here, we show the structural basis for mtPAPs nucleotide
selectivity, dimerization and catalysis. Our structures
reveal an intricate dimerization interface that features an
RNA-recognition module formed through strand
complementation. Further, we propose the structural basis
for the N478D mutation that drastically reduces the length
of poly(A) tails on mitochondrial mRNAs in patients with
spastic ataxia 4 (SPAX4), a severe and progressive
neurodegenerative disease.},
cin = {KI / EMBL / CSSB-KI-MH},
ddc = {540},
cid = {I:(DE-H253)KI-20130912 / I:(DE-H253)EMBL-20120731 /
I:(DE-H253)CSSB-KI-MH-20210520},
pnm = {6215 - Soft Matter, Health and Life Sciences (POF3-621) /
6G3 - PETRA III (POF3-622) / BIOSTRUCT-X - Transnational
access and enhancement of integrated Biological Structure
determination at synchrotron X-ray radiation facilities
(283570)},
pid = {G:(DE-HGF)POF3-6215 / G:(DE-HGF)POF3-6G3 /
G:(EU-Grant)283570},
experiment = {EXP:(DE-H253)P-P14-20150101},
typ = {PUB:(DE-HGF)16},
pubmed = {pmid:26319014},
pmc = {pmc:PMC4605311},
UT = {WOS:000366406500043},
doi = {10.1093/nar/gkv861},
url = {https://bib-pubdb1.desy.de/record/276466},
}